A case of constrictive endocardial sclerosis accompanied with congenital Lutembacher's syndrome.

1865, and detailed report was made by Lutembacher in 1916. The syndrome, a combination of mitral stenosis and atrial septal defect, was at first considered as congenital orign. However, in recent years most of the mitral stenosis in such cases have been considered as acquired origin. Congenital mitral stenosis is a type of the hypoplastic left heart syndrome, and one of the relatively uncommon type of congenital malformation of the heart. A combination of congenital mitral stenosis with atrial septal defect is a more uncommon condition. Endocardial sclerosis or fibroelastosis was assumed to be one of the relatively common causes of cardiac death in infancy,'),') and many cases have been reported in the recent years. Though this disease was recognized as a well-described entity,') extensive morphological varieties corresponding to various nomenclatures such as fetal endocarditis or endomyocarditis,4) primary or prenatal endocardial fibroelastosis,a), f'>,11),12)-24) endocardial dysplasias) and endocardial sclerosis,')'')' 39) are present and the cause and the nature of this disease are still obscure. It is believed that an accumulation of the experiences of many cases will elucidate these